Twenty two patients underwent total anatomic correction of complete atrioventricular septal defect associated with other cardiac anomalies between July 1986 and December 1994 Age ranged from 6 months to 11 years(mean 49.6±35.8 months), and they
composed of 7 males and 15 females. Combined major cardiac anomalies were tetralogy of Fallot(TOF) in 11 cases, double outlet of right ventricle(CORV) in 6 cases, and transposition of great arteries(TGA) in 5 cases. Down's syndrome was associated
in 5
patients with TOF and 1 patient with DORV. They were classified as Rastelli type A in 3 patients, B in 2 patients, and c in 17 patients. Modified Blalock-Taussig shunt was performed in 5 patients and Waterston shunt in l patient as a palliative
procedure. There were 7 perioperative deaths(31.8%) and the causes were pump weaning failure, low cardiac output, acute renal failure, persistant pulmonary hypertension and hypertensive crisis, and sepsis. Reoperations were performed in 4 cases
to
repair atrioventricular valvular regurgitation or to relieve the right ventricular outflo9w tract(RVOT) or pulmonary arterial stenosis. One late death was due to aspiration pneumonia. Second reoperation was necessary for progressive worsening of
left
atrioventricular regurgitation and RVOT stenosis in one patient. Fourteen survived patients were followed up for a mean of 66.0±26.7months and all of them were NYHA functional class I or II.
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